Leiomyosarcoma of the Oropharynx and Neurogenic Tumors in a Young Patient With Turner's Syndrome

نویسندگان

  • Annarosaria De Chiara
  • Gaetano Apice
  • Giustino Silvestro
  • Simona Losito
  • Gerardo Botti
  • Francesco Ionna
  • Vincenzo De Rosa
  • Annamaria Borghese
  • Vito Ninfo
چکیده

PATIENT A case of Turner's syndrome developing a leiomyosarcoma of the oropharynx and metachronous neurogenic tumors (mediastinal 'ganglioneuroblastoma intermixed', subcutaneous neurilemoma) is described. DISCUSSION To our knowledge, this case is the second reported leiomyosarcoma in a patient with Turner's syndrome. Also the site of involvement (palate and oropharynx) is particularly unusual for the already rare leiomyosarcomas in the young age.

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عنوان ژورنال:
  • Sarcoma

دوره 5  شماره 

صفحات  -

تاریخ انتشار 2001